ETHE1 Protein (AA 13-254) (His tag)
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- Target See all ETHE1 Proteins
- ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
- Protein Type
- Recombinant
- Protein Characteristics
- AA 13-254
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Origin
- Human
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Source
- Escherichia coli (E. coli)
- Purification tag / Conjugate
- This ETHE1 protein is labelled with His tag.
- Application
- SDS-PAGE (SDS)
- Characteristics
- ETHE1, 13-254aa, Human, His tag, E.coli
- Purity
- > 90 % by SDS - PAGE
- Top Product
- Discover our top product ETHE1 Protein
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- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- 1.0 mg/ml (determined by Bradford assay)
- Buffer
- Liquid. 20mM Tris-HCl buffer (pH8.0) containing 10% glycerol, 0.1M NaCl
- Storage
- 4 °C
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- Target
- ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
- Alternative Name
- ETHE1 (ETHE1 Products)
- Synonyms
- zgc:85680 Protein, HSCO Protein, YF13H12 Protein, 0610025L15Rik Protein, Hsco Protein, ETHE1, persulfide dioxygenase Protein, ethylmalonic encephalopathy 1 Protein, Ethe1 Protein, ethe1 Protein, ETHE1 Protein
- Background
- ETHE1 is a mitochondrial sulfur dioxygenase involved in catabolism of sulfide that accumulates to toxic levels in ethylmalonic encephalopathy. Mutations of ETHE1 were detected in all the typical ethylmalonic encephalopathy patients analysed, but no ETHE1 mutations were identified in patients presenting with early onset progressive encephalopathy with ethylmalonic aciduria. Recombinant human ETHE1 protein, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography. Synonyms: Protein ETHE1, mitochondrial,. NCBI no.: NP_055112
- Molecular Weight
- 29.1 kDa(267aa) confirmed by MALDI-TOF
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