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Atrophin 1 Products

(Atrophin 1 (ATN1))
Dentatorubral pallidoluysian atrophy (DRPLA) is a rare neurodegenerative disorder characterized by cerebellar ataxia, myoclonic epilepsy, choreoathetosis, and dementia. The disorder is related to the expansion from 7-23 copies to 49-75 copies of a trinucleotide repeat (CAG/CAA) within this gene. The encoded protein includes a serine repeat and a region of alternating acidic and basic amino acids, as well as the variable glutamine repeat. Alternative splicing results in two transcripts variants that encode the same protein. [provided by RefSeq, Feb 2010].

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Featured Atrophin 1 Categories

Atrophin 1 Antibodies

High quality antibodies with extensive validation data.

Atrophin 1 ELISA Kits

Reliable ELISA kits for a wide range of species.

Atrophin 1 Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended Atrophin 1 Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, ELISA, IF
Validations
  • (3)
Cat. No. ABIN560651
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application WB, IP, IHC, ICC
Validations
  • (2)
Cat. No. ABIN7427945
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, ELISA, ICC, IF
Validations
  • (2)
Cat. No. ABIN6256956
Quantity 100 μL
Datasheet Datasheet

Recommended Atrophin 1 ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method
Validations
Cat. No. ABIN1123048
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method
Validations
Cat. No. ABIN1123049
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method
Validations
Cat. No. ABIN1123050
Quantity 96 tests
Datasheet Datasheet

Recommended Atrophin 1 Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1346001
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7418776
Quantity 100 μg
Datasheet Datasheet
Reactivity Mouse
Source Tobacco (Nicotiana tabacum)
Validations
Cat. No. ABIN3131438
Quantity 1 mg
Datasheet Datasheet

Latest Publications for our Atrophin 1 products

Zhang, Xu, Yuan, Sun, Xu: "Epigenetic regulation of Atrophin1 by lysine-specific demethylase 1 is required for cortical progenitor maintenance." in: Nature communications, Vol. 5, pp. 5815, (2014) (PubMed).

Synonyms and alternative names related to Atrophin 1

atrophin 1 (ATN1), atrophin 1 (Atn1), ATN1, Atr1, atrophin-1, B37, D12S755E, DRPLA, Drpla, HRS, NOD, RERE

Protein level used designations for Atrophin 1

  • atrophin-1
  • dentatorubral-pallidoluysian atrophy protein
  • dentatorubral pallidoluysian atrophy
  • dentatorubral-pallidoluysian atrophy protein homolog
  • arginine-glutamic acid dipeptide (RE) repeats
  • atrophin 1
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