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BSND antibody (C-Term)
BSND
Reactivity: Human, Mouse
WB, IHC (p)
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-BSND Antibody
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Target
See all BSND Antibodies
BSND
(Bartter Syndrome, Infantile, with Sensorineural Deafness (Barttin) (BSND))
Binding Specificity
All epitopes for BSND antibodies
AA 291-320, C-Term
Reactivity
All reactivities for BSND antibodies
Human, Mouse
Host
All hosts for BSND antibodies
Rabbit
Clonality
All clonalities for BSND antibodies
Polyclonal
Conjugate
All conjugates for BSND antibodies
This BSND antibody is un-conjugated
Application
All applications for BSND antibodies
Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
Specificity
This antibody reacts to Barttin.
Cross-Reactivity (Details)
Species reactivity (tested):Human and Mouse.
Purification
Affinity chromatography on Protein A
Immunogen
KLH conjugated synthetic peptide between 291~320 amino acids from the C-terminal region of human BSND
Isotype
Ig Fraction
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Alternatives
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Application Details
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Application Notes
Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Handling
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Format
Liquid
Concentration
0.25 mg/mL
Buffer
PBS containing 0.09 % (W/V) sodium azide as preservative
Preservative
Sodium azide
Precaution of Use
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handling Advice
Avoid repeated freezing and thawing.
Storage
4 °C/-20 °C
Storage Comment
Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
Target Details for BSND
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Target
BSND
(Bartter Syndrome, Infantile, with Sensorineural Deafness (Barttin) (BSND))
Alternative Name
Barttin (BSND Products )
Synonyms
BSND antibody, BART antibody, DFNB73 antibody, Bartter syndrome, infantile, with sensorineural deafness (Barttin) antibody, barttin CLCNK type accessory beta subunit antibody, BSND antibody, Bsnd antibody
Background
BSND encodes an essential beta subunit for CLC chloride channels. These heteromeric channels localize to basolateral membranes of renal tubules and of potassium-secreting epithelia of the inner ear.Synonyms: BART, BSND, Bartter syndrome
Gene ID
7809
NCBI Accession
NP_476517
Pathways
Sensory Perception of Sound
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