EHHADH antibody (AA 673-723)

Catalog No. ABIN7451013

Product Details anti-EHHADH Antibody

Target: EHHADH (Enoyl-CoA, Hydratase/3-Hydroxyacyl CoA Dehydrogenase (EHHADH))

Binding Specificity: AA 673-723

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This EHHADH antibody is un-conjugated

Application: Western Blotting (WB), Immunoprecipitation (IP)

Purpose: Rabbit anti-PBE Antibody, Affinity Purified

Predicted Reactivity: Orangutan

Purification: Affinity Purified

Immunogen: between AA 673 and 723

Isotype: IgG

Application Details

Application Notes:

IP: 2 - 10 μg/mg lysate

WB: 1:500 - 1:2,500

Restrictions: For Research Use only

Handling

Concentration: 1000 μg/mL

Buffer: Tris-citrate/phosphate buffer, pH 7 to 8 containing 0.09 % Sodium Azide

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: 4 °C

Expiry Date: 12 months

Target Details for EHHADH

Target: EHHADH (Enoyl-CoA, Hydratase/3-Hydroxyacyl CoA Dehydrogenase (EHHADH))

Alternative Name: PBE (EHHADH Products)

Synonyms: ECHD antibody, L-PBE antibody, LBFP antibody, LBP antibody, PBFE antibody, 1 antibody, Lbp antibody, MEF antibody, Mfe antibody, Mfe1 antibody, Pbe antibody, Pbfe antibody, perMFE-1 antibody, 1300002P22Rik antibody, HD antibody, MFP antibody, MFP1 antibody, zgc:77526 antibody, Ehhadh antibody, enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase antibody, enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase antibody, enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase antibody, peroxisomal bifunctional enzyme-like antibody, EHHADH antibody, ehhadh antibody, Ehhadh antibody, LOC100135519 antibody

Background: Background: Peroxisomal bifunctional enzyme (PBE) is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of PBE contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in the PBE gene are a cause of peroxisomal disorders such as Zellweger syndrome [taken from NCBI Entrez Gene (Gene ID: 1962)].

Gene ID: 1962

NCBI Accession: NP_001957

UniProt: Q08426

Pathways: Monocarboxylic Acid Catabolic Process