FKRP antibody (AA 28-140) (Biotin)

Catalog No. ABIN7153232

Product Details anti-FKRP Antibody (Biotin)

Target: FKRP (Fukutin Related Protein (FKRP))

Binding Specificity: AA 28-140

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This FKRP antibody is conjugated to Biotin

Application: ELISA

Cross-Reactivity: Human

Purification: >95%, Protein G purified

Immunogen: Recombinant Human Fukutin-related protein (28-140AA)

Isotype: IgG

Application Details

Application Notes: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Handling

Format: Liquid

Buffer: Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, pH 7.4

Preservative: ProClin

Precaution of Use: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C,-80 °C

Storage Comment: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.

Target Details for FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Alternative Name: FKRP (FKRP Products)

Background:

Background: Transferase involved in the biosynthesis of the phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-3-N-acetylglucosamine-beta-4-(phosphate-6-)mannose), a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity.

Aliases: Fkrp antibody, FKRP_HUMAN antibody, FLJ12576 antibody, Fukutin related protein antibody, Fukutin-related protein antibody, LGMD2I antibody, MDC1C antibody, MGC2991 antibody

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process