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COX6B1 antibody (AA 1-86)

COX6B1 Reactivity: Human ELISA, IF Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN7149179
  • Target See all COX6B1 Antibodies
    COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))
    Binding Specificity
    • 15
    • 11
    • 8
    • 8
    • 6
    • 2
    • 2
    • 2
    • 1
    • 1
    AA 1-86
    Reactivity
    • 64
    • 7
    • 6
    • 6
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    Human
    Host
    • 58
    • 6
    Rabbit
    Clonality
    • 60
    • 4
    Polyclonal
    Conjugate
    • 24
    • 7
    • 6
    • 6
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This COX6B1 antibody is un-conjugated
    Application
    • 39
    • 31
    • 26
    • 13
    • 13
    • 12
    • 5
    • 3
    • 2
    • 1
    • 1
    ELISA, Immunofluorescence (IF)
    Cross-Reactivity
    Human
    Purification
    >95%, Protein G purified
    Immunogen
    Recombinant Human Cytochrome c oxidase subunit 6B1 protein (1-86AA)
    Isotype
    IgG
    Top Product
    Discover our top product COX6B1 Primary Antibody
  • Application Notes
    Recommended dilution: IF:1:50-1:200,
    Restrictions
    For Research Use only
  • Format
    Liquid
    Buffer
    Preservative: 0.03 % Proclin 300
    Constituents: 50 % Glycerol, 0.01M PBS, PH 7.4
    Preservative
    ProClin
    Precaution of Use
    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Storage
    -20 °C,-80 °C
    Storage Comment
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • Target
    COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))
    Alternative Name
    COX6B1 (COX6B1 Products)
    Synonyms
    COX6B antibody, COXG antibody, COXVIb1 antibody, cox6b antibody, cox6b1 antibody, cox6b1a antibody, coxg antibody, coxvib1 antibody, 2010000G05Rik antibody, Cox6b antibody, RGD1565270 antibody, Cox6b1 antibody, fa92g05 antibody, si:dkey-161j23.2 antibody, wu:fa92g05 antibody, zgc:92631 antibody, COX VIb-1 antibody, COX6B1 antibody, cytochrome c oxidase subunit Vib polypeptide 1 (ubiquitous) antibody, cytochrome c oxidase subunit 6B1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) L homeolog antibody, cytochrome c oxidase, subunit VIb polypeptide 1 antibody, cytochrome c oxidase subunit 6B antibody, cytochrome c oxidase subunit VIb polypeptide 1, pseudogene 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, COX6B protein antibody, cytochrome c oxidase subunit VIb polypeptide 1 antibody, COX6B1 antibody, cox6b1.L antibody, Cox6b1 antibody, Cox6b1-ps1 antibody, LOC100464665 antibody, COX6B antibody, cox6b1 antibody, LOC102143756 antibody
    Background

    Background: Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110], also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.

    Aliases: COX 6B antibody, COX VIb 1 antibody, COX VIb-1 antibody, COX6B antibody, COX6B1 antibody, COXG antibody, COXVIb1 antibody, CX6B1_HUMAN antibody, Cytochrome c oxidase subunit 6B1 antibody, Cytochrome c oxidase subunit VIb antibody, Cytochrome c oxidase subunit VIb isoform 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, Cytochrome c oxidase subunit Vib polypeptide 1 antibody

    UniProt
    P14854
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