ETHE1 antibody

Catalog No. ABIN7255167

Product Details anti-ETHE1 Antibody

Target: ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))

Reactivity: Human, Mouse, Rat

Host: Rabbit

Clonality: Polyclonal

Conjugate: This ETHE1 antibody is un-conjugated

Application: Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)

Characteristics: Polyclonal Antibody

Purification: Affinity purification

Immunogen: Recombinant fusion protein of human ETHE1 (NP_055112.2).

Isotype: IgG

Application Details

Application Notes: WB 1:200-1:1000 IHC 1:50-1:200 IF 1:50-1:200

Restrictions: For Research Use only

Handling

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C. Avoid freeze / thaw cycles.

Target Details for ETHE1

Target: ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))

Alternative Name: ETHE1 (ETHE1 Products)

Synonyms: zgc:85680 antibody, HSCO antibody, YF13H12 antibody, 0610025L15Rik antibody, Hsco antibody, ETHE1, persulfide dioxygenase antibody, ethylmalonic encephalopathy 1 antibody, Ethe1 antibody, ethe1 antibody, ETHE1 antibody

Background: This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms.

Molecular Weight:

Observed_MW: 28 kDa

Calculated_MW: 27 kDa

Gene ID: 23474

UniProt: O95571