Phone:
+1 877 302 8632
Fax:
+1 888 205 9894 (Toll-free)
E-Mail:
orders@antibodies-online.com

MCCC1 antibody

MCCC1 Reactivity: Human, Mouse WB, ELISA, IHC Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN7252978
  • Target See all MCCC1 Antibodies
    MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
    Reactivity
    • 36
    • 19
    • 2
    • 1
    • 1
    • 1
    • 1
    Human, Mouse
    Host
    • 31
    • 6
    Rabbit
    Clonality
    • 34
    • 3
    Polyclonal
    Conjugate
    • 14
    • 7
    • 3
    • 3
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This MCCC1 antibody is un-conjugated
    Application
    • 25
    • 22
    • 4
    • 1
    • 1
    • 1
    Western Blotting (WB), ELISA, Immunohistochemistry (IHC)
    Characteristics
    Polyclonal Antibody
    Purification
    Antigen affinity purification
    Immunogen
    Fusion protein of human MCCC1
    Isotype
    IgG
    Top Product
    Discover our top product MCCC1 Primary Antibody
  • Application Notes
    WB 1:500-1:2000, IHC 1:40-1:200, ELISA 1:5000-1:10000
    Restrictions
    For Research Use only
  • Format
    Liquid
    Concentration
    0.78 mg/mL
    Buffer
    PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4
    Preservative
    Sodium azide
    Precaution of Use
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Storage
    -20 °C
    Storage Comment
    Store at -20°C. Avoid freeze / thaw cycles.
  • Target
    MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))
    Alternative Name
    MCCC1 (MCCC1 Products)
    Synonyms
    MCC-B antibody, MCCA antibody, 1810045E08Rik antibody, 2310058B18Rik antibody, MCCalpha antibody, Mcca antibody, R75106 antibody, methylcrotonoyl-CoA carboxylase 1 antibody, methylcrotonyl-CoA carboxylase alpha chain antibody, methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) antibody, MCCC1 antibody, Mccc1 antibody, MCCA antibody
    Background
    This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.
    Molecular Weight

    Observed_MW: Refer to figures

    Calculated_MW: 80 kDa

    UniProt
    Q96RQ3
You are here:
Support