MCCC1 antibody

Catalog No. ABIN7004181

Product Details anti-MCCC1 Antibody

Target: MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))

Reactivity: Human, Mouse

Host: Rabbit

Clonality: Polyclonal

Conjugate: This MCCC1 antibody is un-conjugated

Application: Western Blotting (WB), ELISA

Characteristics: Polyclonal Antibody

Purification: Antigen affinity purification

Immunogen: Fusion protein of human MCCC1

Isotype: IgG

Application Details

Application Notes: WB 1:500-1:2000, ELISA 1:5000-1:10000

Restrictions: For Research Use only

Handling

Format: Liquid

Concentration: 0.9 mg/mL

Buffer: PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C. Avoid freeze / thaw cycles.

Target Details for MCCC1

Target: MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))

Alternative Name: MCCC1 (MCCC1 Products)

Synonyms: MCC-B antibody, MCCA antibody, 1810045E08Rik antibody, 2310058B18Rik antibody, MCCalpha antibody, Mcca antibody, R75106 antibody, methylcrotonoyl-CoA carboxylase 1 antibody, methylcrotonyl-CoA carboxylase alpha chain antibody, methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) antibody, MCCC1 antibody, Mccc1 antibody, MCCA antibody

Background: This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

Molecular Weight:

Observed_MW: Refer to figures

Calculated_MW: 80 kDa

UniProt: Q96RQ3