×
For best experience we recommend to activate Javascript in your browser.
HADHA antibody (AA 484-763)
HADHA
Reactivity: Human
WB, IHC, IF, IP
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-HADHA Antibody
(hide)
Target
See all HADHA Antibodies
HADHA
(Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
Binding Specificity
All epitopes for HADHA antibodies
AA 484-763
Reactivity
All reactivities for HADHA antibodies
Human
Host
All hosts for HADHA antibodies
Rabbit
Clonality
All clonalities for HADHA antibodies
Polyclonal
Conjugate
All conjugates for HADHA antibodies
This HADHA antibody is un-conjugated
Application
All applications for HADHA antibodies
Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF), Immunoprecipitation (IP)
Sequence
IAAVSKRPEK VIGMHYFSPV DKMQLLEIIT TEKTSKDTSA SAVAVGLKQG KVIIVVKDGP GFYTTRCLAP MMSEVIRILQ EGVDPKKLDS LTTSFGFPVG AATLVDEVGV DVAKHVAEDL GKVFGERFGG GNPELLTQMV SKGFLGRKSG KGFYIYQEGV KRKDLNSDMD SILASLKLPP KSEVSSDEDI QFRLVTRFVN EAVMCLQEGI LATPAEGDIG AVFGLGFPPC LGGPFRFVDL YGAQKIVDRL KKYEAAYGKQ FTPCQLLADH ANSPNKKFYQ
Cross-Reactivity
Human, Mouse
Characteristics
Polyclonal Antibodies
Purification
Affinity purification
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 484-763 of human HADHA (NP_000173.2).
Isotype
IgG
Alternatives
(show)
Application Details
(hide)
Application Notes
WB,1:500 - 1:2000,IHC,1:50 - 1:200,IF,1:50 - 1:200,IP,1:50 - 1:200
Restrictions
For Research Use only
Handling
(hide)
Format
Liquid
Buffer
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
Preservative
Sodium azide
Precaution of Use
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
Store at -20°C. Avoid freeze / thaw cycles.
Target Details for HADHA
(hide)
Target
HADHA
(Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
Alternative Name
HADHA (HADHA Products )
Synonyms
cb1055 antibody, hadha antibody, im:7136067 antibody, wu:fa14c08 antibody, ECHA antibody, GBP antibody, HADH antibody, LCEH antibody, LCHAD antibody, MTPA antibody, TP-ALPHA antibody, RGD1560655 antibody, C77020 antibody, Mtpa antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antibody, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antibody, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antibody, HADHA antibody, hadha antibody, hadha.S antibody, hadhaa antibody, Hadha antibody
Background
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.,HADHA,ECHA,GBP,HADH,LCEH,LCHAD,MTPA,TP-ALPHA,Cancer,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Lipid Metabolism,Cardiovascular,Lipids,Fatty Acids,HADHA
Molecular Weight
28 kDa/83 kDa
Gene ID
3030
UniProt
P40939
Pathways
Monocarboxylic Acid Catabolic Process
Recently viewed
(hide)