Dysferlin antibody (C-Term)
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- Target See all Dysferlin (DYSF) Antibodies
- Dysferlin (DYSF)
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Binding Specificity
- C-Term
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Reactivity
- Human
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Host
- Rabbit
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Clonality
- Polyclonal
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Conjugate
- This Dysferlin antibody is un-conjugated
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Application
- Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
- Specificity
- This antibody reacts to Dysferlin, Limb Girdle Muscular Dystrophy 2b (AUTOSOMAL RECESSIVE) (DYSF).
- Purification
- Immunoaffinity Chromatography
- Immunogen
- A synthetic peptide corresponding to C-terminal of human Dysferlin Genename: DYSF
- Isotype
- IgG
- Top Product
- Discover our top product DYSF Primary Antibody
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- Application Notes
- Optimal working dilution should be determined by the investigator.
- Restrictions
- For Research Use only
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- Buffer
- 10 mM PBS, pH 7.4 containing BSA as stabilizer and 0,09 % sodium azide as preservative
- Preservative
- Sodium azide
- Precaution of Use
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Storage
- 4 °C
- Storage Comment
- Store the antibody undiluted at 2-8 °C. DO NOT FREEZE!
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- Target
- Dysferlin (DYSF)
- Alternative Name
- Dysferlin (DYSF Products)
- Synonyms
- DYSF antibody, fb73b05 antibody, wu:fb73b05 antibody, si:rp71-50c18.1 antibody, DKFZp459E1226 antibody, 2310004N10Rik antibody, AI604795 antibody, D6Pas3 antibody, mFLJ00175 antibody, FER1L1 antibody, LGMD2B antibody, MMD1 antibody, dysferlin antibody, dysferlin, limb girdle muscular dystrophy 2B (autosomal recessive) antibody, myoferlin antibody, DYSF antibody, dysf antibody, LOC589501 antibody, Dysf antibody
- Background
- Dysferlin is the protein product of the 2p13 gene that is defective in patients with Limb-Girdle Muscular Dystrophy type 2B (LGMD2B) and Miyoshi Myopathy (MM). Dysferlin is normally localized to the muscle plasma membrane. In patients with LGMD2B and MM, immunoreactivity to dysferlin is severely reduced or lost, depending on the type of mutation. This antibody is used for the characterization of LGMD2B and MM.Synonyms: DYSF, Dystrophy-associated fer-1-like protein, FER1L1, Fer-1-like protein 1
- Gene ID
- 8291
- NCBI Accession
- NP_001123927
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