Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Buffer
In 1x PBS, pH 7.4
Handling Advice
Aliquot to avoid repeated freezing and thawing.
Storage
-20 °C
Storage Comment
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
Kotarsky, Karikoski, Mörgelin, Marjavaara, Bergman, Zhang, Smet, van Coster, Fellman: "Characterization of complex III deficiency and liver dysfunction in GRACILE syndrome caused by a BCS1L mutation." in: Mitochondrion, Vol. 10, Issue 5, pp. 497-509, (2010) (PubMed).
Gil-Borlado, González-Hoyuela, Blázquez, García-Silva, Gabaldón, Manzanares, Vara, Martín, Seneca, Arenas, Ugalde: "Pathogenic mutations in the 5' untranslated region of BCS1L mRNA in mitochondrial complex III deficiency." in: Mitochondrion, Vol. 9, Issue 5, pp. 299-305, (2009) (PubMed).