FKRP antibody (AA 237-265)
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- Target See all FKRP Antibodies
- FKRP (Fukutin Related Protein (FKRP))
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Binding Specificity
- AA 237-265
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Reactivity
- Human
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Host
- Rabbit
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Clonality
- Polyclonal
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Conjugate
- This FKRP antibody is un-conjugated
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Application
- Western Blotting (WB)
- Purification
- This antibody is purified through a protein A column, followed by peptide affinity purification.
- Immunogen
- This FKRP antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 237-265 amino acids from the Central region of human FKRP.
- Isotype
- Ig Fraction
- Top Product
- Discover our top product FKRP Primary Antibody
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- Application Notes
- For WB starting dilution is: 1:1000
- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- 0.5 mg/mL
- Buffer
- Supplied in PBS with 0.09 % (W/V) sodium azide.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Storage
- 4 °C,-20 °C
- Storage Comment
- Store at 4°C for three months and -20°C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
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- Target
- FKRP (Fukutin Related Protein (FKRP))
- Alternative Name
- FKRP (FKRP Products)
- Synonyms
- zgc:162829 antibody, LGMD2I antibody, MDC1C antibody, MDDGA5 antibody, MDDGB5 antibody, MDDGC5 antibody, A830029B19Rik antibody, AI842067 antibody, AI847300 antibody, LGMD1I antibody, fukutin related protein antibody, FKRP antibody, fkrp antibody, Fkrp antibody
- Background
- This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].
- Molecular Weight
- 55 kDa
- Gene ID
- 79147
- UniProt
- Q9H9S5
- Pathways
- Regulation of Carbohydrate Metabolic Process
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