OPA3 antibody (C-Term)
-
- Target See all OPA3 Antibodies
- OPA3 (Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3))
-
Binding Specificity
- C-Term
-
Reactivity
- Human, Pig
-
Host
- Rabbit
-
Clonality
- Polyclonal
-
Conjugate
- This OPA3 antibody is un-conjugated
-
Application
- Western Blotting (WB)
- Sequence
- SCLMLEYWRH QLQQRRKEKE RRVAREALRG EVGHLGLALE ELQAQVQATS
- Predicted Reactivity
- Human: 100%, Pig: 82%
- Characteristics
- This is a rabbit polyclonal antibody against OPA3. It was validated on Western Blot.
- Purification
- Affinity Purified
- Immunogen
- The immunogen is a synthetic peptide directed towards the C terminal region of human OPA3
- Top Product
- Discover our top product OPA3 Primary Antibody
-
-
- Application Notes
- Optimal working dilutions should be determined experimentally by the investigator.
- Comment
-
Antigen size: 180 AA
- Restrictions
- For Research Use only
-
- Format
- Liquid
- Concentration
- Lot specific
- Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Handling Advice
- Avoid repeated freeze-thaw cycles.
- Storage
- -20 °C
- Storage Comment
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
-
- Target
- OPA3 (Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3))
- Alternative Name
- OPA3 (OPA3 Products)
- Synonyms
- D630048P19Rik antibody, Gm1425 antibody, Gm472 antibody, MGA3 antibody, optic atrophy 3 antibody, OPA3, outer mitochondrial membrane lipid metabolism regulator antibody, opa3 antibody, Opa3 antibody, OPA3 antibody
- Background
-
The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Mutations in this gene have been shown to result in 3-methylglutaconic aciduria type III and autosomal dominant optic atrophy and cataract. Multiple transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: FLJ22187, FLJ25932, MGA3, MGC75494
Protein Interaction Partner: PRMT6, KDM1A, SUV39H1, APP,
Protein Size: 180 - Molecular Weight
- 20 kDa
- Gene ID
- 80207
- NCBI Accession
- NM_001017989, NP_001017989
- UniProt
- Q9H6K4
-