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BCKDHB antibody (N-Term)

BCKDHB Reactivity: Human, Rat, Cow, Dog, Horse, Pig, Rabbit WB Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN2787755
  • Target See all BCKDHB Antibodies
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Binding Specificity
    • 8
    • 8
    • 7
    • 1
    • 1
    N-Term
    Reactivity
    Human, Rat, Cow, Dog, Horse, Pig, Rabbit
    Host
    • 18
    Rabbit
    Clonality
    • 18
    Polyclonal
    Conjugate
    • 8
    • 2
    • 2
    • 2
    • 2
    • 2
    This BCKDHB antibody is un-conjugated
    Application
    • 18
    • 14
    • 14
    • 14
    • 13
    • 5
    • 3
    • 1
    Western Blotting (WB)
    Sequence
    GFLHPAATVE DAAQRRQVAH FTFQPDPEPR EYGQTQKMNL FQSVTSALDN
    Predicted Reactivity
    Cow: 93%, Dog: 93%, Horse: 93%, Human: 100%, Pig: 86%, Rabbit: 93%, Rat: 79%
    Characteristics
    This is a rabbit polyclonal antibody against BCKDHB. It was validated on Western Blot.
    Purification
    Affinity Purified
    Immunogen
    The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB
    Top Product
    Discover our top product BCKDHB Primary Antibody
  • Restrictions
    For Research Use only
  • Format
    Liquid
    Concentration
    1 mg/mL
    Buffer
    Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
    Preservative
    Sodium azide
    Precaution of Use
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Handling Advice
    Avoid repeat freeze-thaw cycles.
    Storage
    -20 °C
    Storage Comment
    For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
  • Target
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Alternative Name
    BCKDHB (BCKDHB Products)
    Synonyms
    zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
    Background
    Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform.
    Protein Interaction Partner: CUL3, BCKDHA,
    Protein Size: 218
    Molecular Weight
    23 kDa
    Gene ID
    594
    UniProt
    Q5T2J3
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